Management of Short-Segment Hirschsprung-Associated Enterocolitis in an Infant in East Kalimantan, Indonesia: A Case Report
DOI:
https://doi.org/10.59141/-.v8i2.552Keywords:
Hirschsprung Disease, Hirschsprung-Associated Enterocolitis, InfantAbstract
Hirschsprung’s disease (HD) is a congenital disorder characterized by the absence of ganglion cells in the Meissner’s and Auerbach’s plexuses. The incidence of HD has been reported to be higher in Asian infants; nevertheless, HD cases in Indonesia remain underexamined. Delayed diagnosis places neonatal patients with HD at a 13-fold increased risk of developing Hirschsprung-associated enterocolitis (HAEC) preoperatively, which may be a life-threatening condition. A 51-day-old female infant was brought to the emergency room with abdominal distension and vomiting, and had bowel movements only 1–2 times per week, with an estimated volume of approximately 5 cc per episode. Radiographic examination showed a narrowed sigmoid colon and constriction of the rectosigmoid region, accompanied by proximal colonic dilatation. A HAEC score was calculated, yielding a result of 14, consistent with Hirschsprung-associated enterocolitis. Management in this case followed the American Pediatric Surgical Association Board of Governors Guidelines. A transanal Swenson procedure with frozen section biopsy was performed, and intraoperative findings confirmed short-segment Hirschsprung-associated enterocolitis. The diagnosis and patient management were carried out appropriately in accordance with established guidelines and clinical standards.
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Copyright (c) 2026 Megaria Sihombing, Santi Rini, Nisa Alyananda Ritonga, Sonia Edna Rumondang, Nurmasithah Nurmasithah
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